まとめ
マルチセントリックカステルマン病は攻撃的ですが,1人の患者は治療に良好な反応を示しました. プレドニゾーンとレチノ酸は,このまれな状態の治療に成功した治療法を提供しました.
科学分野:
- 腫瘍学 腫瘍学
- 血液学 ヘマトロジ
- 免疫学 免疫学とは
背景:
- 多中心性カステルマン病 (MCD) は,珍しいリンパ増殖性疾患である.
- MCDは通常,攻撃的な臨床行動と悪い予後を示します.
- MCDの現在の治療戦略は,決定的な有効性が欠けている.
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