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Updated: Jul 16, 2026

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase (COX/SDH) Double-labeling Histochemistry
06:53

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase (COX/SDH) Double-labeling Histochemistry

Published on: November 23, 2011

ミトコンドリア呼吸器連鎖疾患II:神経変性疾患と核遺伝子の欠陥

J V Leonard1, A H Schapira

  • 1Biochemistry, Endocrine and Metabolic Unit, Institute of Child Health, London, UK.

Lancet (London, England)
|February 9, 2000
PubMed
まとめ

このレビューは,神経退行性疾患に焦点を当てて,酸化性リン酸化 (OXPHOS) システムにおける核コード化された欠陥をカバーしています. 核遺伝子の突然変異がどのようにOXPHOS欠乏症とインパクトアポトーシスにつながるかを探求しています.

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