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Updated: Jul 18, 2026

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase (COX/SDH) Double-labeling Histochemistry
06:53

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase (COX/SDH) Double-labeling Histochemistry

Published on: November 23, 2011

ミトコンドリア呼吸器連鎖障害 I:ミトコンドリアDNAの欠陥

J V Leonard1, A H Schapira

  • 1Biochemistry, Endocrine and Metabolic Unit, Institute of Child Health, London, UK.

Lancet (London, England)
|February 16, 2000
PubMed
まとめ

ミトコンドリアDNA (mtDNA) 変異または外部毒素によって引き起こされるミトコンドリア機能障害は,神経変性疾患を含む様々な疾患を引き起こす. これらの酸化リン酸化 (OXPHOS) 欠陥を理解することは,疾患の治療に極めて重要です.

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