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Updated: Jul 16, 2026

Method of Direct Segmental Intra-hepatic Delivery Using a Rat Liver Hilar Clamp Model
09:22

Method of Direct Segmental Intra-hepatic Delivery Using a Rat Liver Hilar Clamp Model

Published on: April 2, 2017

ウィルソン病の患者の肝臓における酸化リン酸化欠陥

M Gu1, J M Cooper, P Butler

  • 1University Department of Clinical Neurosciences, Royal Free and University College Medical School, and Institute of Neurology, London, UK.

Lancet (London, England)
|September 12, 2000
PubMed
まとめ

ウィルソン病 (WD) は銅の堆積を伴うもので,肝臓における重度のミトコンドリア機能障害を引き起こす. このエネルギー代謝の欠陥は,酸化的ダメージがWDの鍵であることを示唆し,抗酸化剤療法研究を支援しています.

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