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James K Stoller1, Loutfi S Aboussouan

  • 1Department of Pulmonary, Allergy, and Critical Care Medicine, Cleveland Clinic Foundation, 9500 Euclid Avenue, Cleveland, OH 44195, USA. stollej@ccf.org

PubMed
まとめ

アルファ1-アンチトリプシン欠乏症 (AATD) は,肝臓および肺疾患を引き起こす遺伝疾患です. プラズマ由来療法によるAAT濃度の上昇は,AATD患者の肺機能低下を遅らせる可能性があります.

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