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Updated: Jul 12, 2026

Fractionation for Resolution of Soluble and Insoluble Huntingtin Species
07:08

Fractionation for Resolution of Soluble and Insoluble Huntingtin Species

Published on: February 27, 2018

ヒトシスティノシス:シスタインの細胞内堆積

K Hummeler, B A Zajac, M Genel

    Science (New York, N.Y.)
    |May 15, 1970
    PubMed
    まとめ

    システノシスは,直腸粘膜,白血球,および線維芽細胞内のリソソームにシスティンの蓄積を引き起こします. これらの膜に結合したインクルージョンは,無形または結晶化されたシスティンを含んでおり,酸ホスファターゼの活動により,リゾソームとして識別されます.

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