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Updated: Jul 10, 2026

Cystic Fibrosis Aggregate Biofilm Model to Study Infection-relevant Gene Expression
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Cystic Fibrosis Aggregate Biofilm Model to Study Infection-relevant Gene Expression

Published on: April 18, 2025

大人のシスティック・フィブロシスが発症します

Michael P Boyle1

  • 1Johns Hopkins Adult Cystic Fibrosis Program, Division of Pulmonary and Critical Care Medicine, Johns Hopkins University School of Medicine, Baltimore, Maryland, USA. mboyle@jhmi.edu

JAMA
|October 18, 2007
PubMed
まとめ

囊性線維症 (Cystic fibrosis,CF) は,複数の臓器,主に肺と臓に影響を与える遺伝疾患です. 治療の進歩により,生存率が著しく増加し,現在,CFを患っている成人の数が増加しています.

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