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Updated: Jun 27, 2026

Detecting Glycogen in Peripheral Blood Mononuclear Cells with Periodic Acid Schiff Staining
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Detecting Glycogen in Peripheral Blood Mononuclear Cells with Periodic Acid Schiff Staining

Published on: December 23, 2014

SRC-2コアクティベーターの欠如は,フォン・ジャーケ病に似たグリコゲノパシーを引き起こす

Atul R Chopra1, Jean-Francois Louet, Pradip Saha

  • 1Department of Molecular and Cellular Biology, Baylor College of Medicine, 1 Baylor Plaza, Houston, TX 77030, USA.

Science (New York, N.Y.)
|November 29, 2008
PubMed
まとめ

転写共活性化剤SRC-2は,G6Pase酵素を調節することによって,肝臓のグルコース生成を制御する. マウスのSRC-2欠乏症はフォン・ジャーケを模倣している.

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