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Genetic Analysis of Hereditary Transthyretin Ala97Ser Related Amyloidosis
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トランスチレチン関連の心臓アミロイドーシスと軽鎖性心臓アミロイドーシスにおける左心室の構造と機能

Candida Cristina Quarta1, Scott D Solomon, Imran Uraizee

  • 1Cardiovascular Division (C.C.Q., S.D.S., I.U.), Brigham and Women's Hospital, Harvard Medical School, Boston, MA; Institute of Cardiology (C.C.Q., S.L., M.F., C.G., A.M., C.R.), University of Bologna and S.Orsola-Malpighi Hospital, Bologna, Italy; Department of Cardiology (J.K., R.H.F.), Harvard Vanguard Medical Associates, Boston, MA; and Brigham and Women's Hospital Cardiac Amyloidosis Program (R.H.F), Harvard Medical School, Boston, MA.

Circulation
|February 25, 2014
PubMed
まとめ

心臓アミロイドーシス (CA) の予後は,タイプによって異なります. トランスチレチン (TTR) CAは,類似の左心室ストレイン障害にもかかわらず,免疫グロブリン軽鎖 (AL) CAよりも優れた生存率を有しており,ユニークなAL毒性メカニズムを示唆しています.

キーワード:
アミロイドアミロイドとはアミロイドーシス,遺伝性,トランスチレチン関連心筋病変症は,心筋病変症である.エコーカルディオグラフィー エコーカルディオグラフィートランスチレチネン (トランスチレチネン)

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