子供 の 心筋 病 症: 分類 と 診断: アメリカ 心臓 協会 の 科学 的 な 声明
Circulation
|May 29, 2019
まとめ
小児心筋病は 深刻な心筋疾患で より良い診断方法が必要です 早期の診断と研究は 罹患児の成果と生活の質の改善に不可欠です
科学分野:
- 小児心臓科
- 心筋病の研究
- 心臓 疾患 の 遺伝
背景:
- 診断から2年以内に40%近くが死亡し,心臓移植が必要となる.
- 1歳以上の子どもの心臓移植の主な原因は小児心筋疾患で 過去10年間で心臓移植の割合は減少していません
- 重要な影響があるにもかかわらず,小児心筋病の研究と集中は,比較可能な小児がんに遅れをとっています.
研究 の 目的:
- 子どもの心筋病の原因について 最新の理解を提供するためです
- 小児心筋病の最適な診断方法を概説する.
- 早期診断と小児心筋病の改善のための将来の研究優先事項を導き出す.
主な方法:
- 小児心筋病に関する現在の科学的理解と専門家のコンセンサスの見直し
- 国立心臓・肺・血液研究所が 資金提供する小児心筋病登録のデータ分析
- 診断基準と小児心筋病症の分類に重点を置く
主要な成果:
- ほとんどの小児心筋病の症例では遺伝的原因が疑われるが,ごく少数の症例では確定している.
- 小児心筋病の発生率は約10万人に1人です.
- 現在の診断理解と研究努力は,病状の深刻さからして不十分です.
結論:
- 小児心筋病の診断と分類に 焦点を合わせることが不可欠です
- 早期診断と標的型の研究は,臨床結果と生活の質を改善するために不可欠です.
- この声明は,小児心筋病によって引き起こされる課題に対処するための将来の研究を刺激することを目的としています.
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