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Updated: Jul 16, 2025

SorLA and CLC:CLF-1-dependent Downregulation of CNTFRα as Demonstrated by Western Blotting, Inhibition of Lysosomal Enzymes, and Immunocytochemistry
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SorLA and CLC:CLF-1-dependent Downregulation of CNTFRα as Demonstrated by Western Blotting, Inhibition of Lysosomal Enzymes, and Immunocytochemistry

Published on: January 6, 2017

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バッテン病の遺伝子産物CLN5は,リソソーマルビス ((monoacylglycero) リン酸合成体である

Uche N Medoh1,2,3,4, Andy Hims1,2,3, Julie Y Chen1,2,3

  • 1Department of Chemical Engineering, Stanford University, Stanford, CA 94305, USA.

Science (New York, N.Y.)
|September 14, 2023
PubMed
まとめ

科学者は,CLN5が,リスソームの機能と神経変性防止に不可欠な脂質であるビス・モノアシルグリセロフォスファート (BMP) を合成する酵素であることを発見しました.

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