ラプンツェル症候群 複数の同時に内分泌する場所
Eric C Morey1, Caitlin Brandle1, Stephen Schaffner1
1Radiology, Augusta University Medical College of Georgia, Augusta, USA.
Cureus
|August 27, 2025
まとめ
ラプンツェル症候群は 胃のトリコベゾアを含む珍しい疾患で 自閉症の子供に診断されました この重度の胃腸合併症の治療には 早期の手術が不可欠です
科学分野:
- 小児胃腸内科
- 手術 症例 報告
背景:
- ラプンツェル症候群は 稀な胃トリコベゾアで 細腸に広がっています
- トリコチロマニアとトリコファギアを患う少女の女性で最もよく見られる.
研究 の 目的:
- パイカとトリコチロマニアの 非言語自閉症の子供の ラプンツェル症候群の ユニークな症例を紹介します
- 腹部コンピュータトモグラフィー (CT) の診断的有用性を強調する.
- ラプンツェル症候群の早期手術の重要性を強調する
主な方法:
- 9歳の女の子は 言語障害の自閉症とピカとトリコチロマニアで 急性腹痛と嘔吐を呈しました
- 腹部コンピュータトモグラフィー (CT) により,小腸-小腸の多発性腸内が明らかになった.
- 患者はベゾアを摘出するために開いた腹腔切開術を受けた.
主要な成果:
- 大量の胃腸トライコベゾアは 開放式腹腔切除で成功しました
- 患者は手術後の症状の解消を経験しました.
- このケースは,重度のベゾア病と関連した広範な放射線学的発見を示した.
結論:
- ラプンツェル症候群は神経発達障害や ピカやトリコチロマニアのような 行動性併発症の子供でも発生します
- 腹部CTは,広範囲のトリコベゾアの診断と外科的管理の計画に不可欠です.
- 重篤な合併症を予防し,ラプンツェル症候群の罹患率を減らすために,迅速な手術は不可欠です.
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