生まれながらの血栓性血栓性紫外線の再発と臓器不全を減らすためにADAMTS13の予防を最適化

Bérangère S Joly1, Adrien Joseph2, Raïda Bouzid3

  • 1Service d'Hématologie biologique, Hôpital Lariboisière, AP-HP. Nord, Université Paris Cité, Paris & INSERM UMRS1138, Centre de Recherche des Cordeliers, Université Paris Cité, Sorbonne Université, Paris, France, France.

Blood advances
|August 28, 2025
PubMed
まとめ

生まれながらの血栓性血栓縮小性紫外線 (cTTP) は,集中予防が必要である. 再結合ADAMTS13は安全で効果的な選択肢であり, 再発のない生存率を向上させ, 장기損傷を減らすことができます.

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