偶然 の 転落 が 珍しい 病気 の 非 典型 的 な 発現 を 明らか に し た:バッド ・ チアリ 症候群 の 症例
Sneha Celine Jossie1, Thuraya Al Bhaisi1, Farooq Khan1
1Internal Medicine, King's College Hospital London, Dubai, ARE.
Cureus
|September 2, 2025
まとめ
肝臓の静脈流出阻害であるバッド・キアリ症候群 (BCS) は,多細胞血症 (PV) の患者で偶然診断された. 早期診断と多科目の治療は この珍しい血管疾患の 管理に不可欠です
科学分野:
- ヘパトロジー
- 血管医学
- 血液学
背景:
- バド・キアリ症候群 (BCS) は希少な肝臓静脈流出阻害である.
- 多細胞血症 (PV) は,BCSの頻繁な根本的な原因です.
- メタボリック機能障害に関連した脂肪肝炎 (MASH) の診断は,現在の基準に照らして慎重に検討する必要があります.
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