デスモソーム性不律性心筋病における運動ストレステストの診断および予後的重要性

Matteo Castrichini1, Raquel Neves1, Ramin Garmany2

  • 1Department of Cardiovascular Medicine, Division of Heart Rhythm Services and the Windland Smith Rice Genetic Heart Rhythm Clinic, Mayo Clinic, Rochester, Minnesota, USA; Department of Molecular Pharmacology and Experimental Therapeutics, Windland Smith Rice Sudden Cardiac Death Genomics Laboratory, Mayo Clinic, Rochester, Minnesota, USA.

PubMed
まとめ

PKP2発心筋不全 (PKM) 患者における運動ストレステスト (EST) 中の不律症は,特に回復期において,大動脈不律症 (MVA) の事象を予測する. これは,PKP2-ACMにおけるリスクの階層化における ESTの重要性を強調しています.

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