複雑な上腸間膜動脈症候群

Superior mesenteric artery syndrome (SMA) is a rare condition more commonly seen in young, thin females. In SMA syndrome, the duodenum is compressed between the SMA and the aorta, and the patient presents with obstructive symptoms. Here, we present a case of complicated SMA syndrome in a young patient with limited scleroderma. She presented with abdominal pain, early satiety, and significant weight loss. Her condition was further complicated by the development of emphysema. This case illustrates the diagnostic challenge and complexity of managing SMA syndrome in the context of connective tissue disorders with multisystemic manifestations.