原発性シェーグレン症候群の思春期発症例:症例報告
Sutlan Albaqawi1, Ahmed Alanazi1, Ruqayyah H Almarshadi1
1Oral and Maxillofacial Surgery, King Khalid Hospital, Hail, SAU.
Cureus
|December 22, 2025
まとめ
小児における若年発症原発性シェーグレン症候群はまれであり、唾液腺腫脹や口腔乾燥などの異常な症状を呈することが多い。唾液腺生検による早期診断は、永続的な損傷を防ぐために重要である。
背景:
- 原発性シェーグレン症候群(pSS)は、主に成人を侵す自己免疫疾患である。
- 小児患者における若年発症pSSは例外的にまれであり、非典型的な症状を呈することが多い。
- 小児における診断の遅れは、永続的な腺損傷や全身性合併症を含む重大な罹患につながる可能性がある。
結論:
- 小児原発性シェーグレン症候群は、そのまれな発生率と非典型的な提示のため、高い臨床的疑いが必要である。
- 小唾液腺生検は、小児における診断を確認するための有用なツールである。
- 長期的な合併症を軽減するためには、早期の特定と介入が不可欠である。
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