重症大動脈弁上狭窄症に対するダブルパッチ大動脈形成術：症例報告

Severe supravalvular aortic stenosis in a young patient is a rare but critical condition requiring timely diagnosis and intervention. We report a 15-year-old girl presenting with exertional dyspnea, chest pain, and palpitations. Echocardiography and multidetector computed tomography (MDCT) confirmed severe supravalvular aortic stenosis, myxomatous mitral valve with moderate to severe mitral regurgitation, and reduced ejection fraction. A double patch aortoplasty was performed with a successful outcome. This case underscores the importance of early diagnosis and tailored surgical intervention along with continued monitoring during follow up visits in managing complex congenital heart disease (CHD) diagnosed at an early age.