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Updated: Sep 8, 2026

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy
07:45

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy

Published on: October 21, 2014

球状白血病のチューブル:右手のヘリックス

E J Yunis, R E Lee

    Science (New York, N.Y.)
    |July 3, 1970
    PubMed
    まとめ

    グローボイド白血病とゴッシャー病は,似たようなサイトプラズマ管の構造を共有しています. この形態学的類似性は,球状細胞におけるセレブロサイドの蓄積を示唆し,これらの神経学的障害を理解するための重要な発見である.

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