急性ポルフィア発作の予防は,静脈内注射ヘマチンによるものです
Lancet (London, England)
|September 2, 1978
まとめ
毎週静脈内注入するヘマチン注入は,毎月の急性中断性ポルフィリア (AIP) の発作を効果的に予防しました. 女性の患者で. 発作は治療を中止した後に再発し,ヘマチナインが顕著になった.
科学分野:
- バイオケミストリー バイオケミストリー
- 遺伝学 遺伝学とは
- 内科内科は,内科の内科である.
背景:
- 急性中断性ポルフィリア (A.I.P.) 希少な遺伝疾患である.
- A.I.P. (アライプ) とは 発作はしばしばホルモンの変動,特に月経に関連しています.
- 現在の治療法は,症状を管理し,発作を予防することを目的としています.
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