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Updated: Jul 18, 2026

Visualization of Mitochondrial Respiratory Function using Cytochrome C Oxidase / Succinate Dehydrogenase (COX/SDH) Double-labeling Histochemistry
06:53

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Published on: November 23, 2011

线粒体呼吸链疾病 I:线粒体DNA缺陷

J V Leonard1, A H Schapira

  • 1Biochemistry, Endocrine and Metabolic Unit, Institute of Child Health, London, UK.

Lancet (London, England)
|February 16, 2000
PubMed
概括

线粒体功能障碍是由线粒体DNA (mtDNA) 突变或外部毒素引起的,导致各种疾病,包括神经退行性疾病. 了解这些氧化酸化 (OXPHOS) 缺陷对于疾病治疗至关重要.

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