一个BBS蛋白质的核心复合体与GTPase Rab8合作,促进纤毛膜生物发生

Maxence V Nachury1, Alexander V Loktev, Qihong Zhang

  • 1Genentech, Inc., South San Francisco, CA 94080, USA. nachury@gene.com

Cell
|June 19, 2007
PubMed
概括

巴德特-比德尔综合征 (BBS) 综合体,称为BBSome,对于初级毛形成至关重要. 这个复合体中的缺陷会破坏囊泡运输,导致BBS症状.

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