解读异常性炎症性肌肉病变的临床表现,病变发生和治疗
Lisa G Rider1, Frederick W Miller
1Environmental Autoimmunity Group, Program of Clinical Research, National Institute of Environmental Health Sciences, National Institutes of Health, US Department of Health and Human Services, Bethesda, Maryland 20892, USA. riderl@mail.nih.gov
JAMA
|January 13, 2011
概括
异常性炎症性肌肉病变,包括多质神经炎和皮肤神经炎,是导致肌肉衰弱的自身免疫性疾病. 将这些肌肉炎综合征分为不同的表型有助于预测患者的结果和指导治疗策略.
科学领域:
- 类风湿病学 类风湿病学
- 免疫学 免疫学 免疫学
- 神经学 神经学
背景情况:
- 异常性炎症性肌肉病变 (IIM) 是一种系统性自身免疫性疾病,其特征是慢性肌肉衰弱和炎症.
- 常见的形式包括多聚肌炎,皮肤肌炎和包容体肌炎,导致显著的发病率和死亡率.
- IIM的病因在很大程度上是未知的.
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