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左心室结构和功能在与甲胺相关的与轻链心脏氨基粉症的比较

Candida Cristina Quarta1, Scott D Solomon, Imran Uraizee

  • 1Cardiovascular Division (C.C.Q., S.D.S., I.U.), Brigham and Women's Hospital, Harvard Medical School, Boston, MA; Institute of Cardiology (C.C.Q., S.L., M.F., C.G., A.M., C.R.), University of Bologna and S.Orsola-Malpighi Hospital, Bologna, Italy; Department of Cardiology (J.K., R.H.F.), Harvard Vanguard Medical Associates, Boston, MA; and Brigham and Women's Hospital Cardiac Amyloidosis Program (R.H.F), Harvard Medical School, Boston, MA.

Circulation
|February 25, 2014
PubMed
概括

心脏粉症 (CA) 的预后因类型而异. 尽管有类似的左心室应变损伤,但Transthyretin (TTR) CA的存活率优于免疫球蛋白轻链 (AL) CA,这表明了独特的AL毒性机制.

关键词:
氨基化物 氨基化物氨基粉症,遗传性,与甲胺相关的.心肌病心脏病变的发生.超声心电图 (Echocardiography) 是一种心声回声仪.转胺素是什么意思

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