热带内肌纤维化:自然史,挑战和前景
Antonio Grimaldi1, Ana Olga Mocumbi1, Juergen Freers1
1From Cardiovascular and Thoracic Department, San Raffaele Hospital, Milan, Italy (A.G.); St. Raphael of St. Francis Nsambya Hospital, Kampala, Uganda (A.G.); Paris Cardiovascular Research Center (INSERM U970), Cardiology & Development, Paris, France (M.M., K.N., X.J., E.M.); Instituto Nacional de Saúde, Maputo, Mozambique (A.O.M.); Division of Cardiology, Department of Medicine, Makerere University, Kampala, Uganda (J.F.); Institut du Thorax, Nantes, France (M.L.); Maputo Heart Institute, Maputo, Mozambique (M.L., B.F., D.S., X.J., E.M.); European Georges Pompidou Hospital, Cardiology Department, Paris, France (M.M., X.J., E.M.); Necker Enfants Malades Hospital, Pediatric Cardiology, Paris, France (D.S.); Maxcure Hospitals, Hyderabad, India (K.N.); Sydney Medical School, Sydney, Australia (D.S.C.); and Paris Descartes University, Paris, France (D.S., X.J., E.M.).
热带内肌纤维化 (EMF) 是一种严重的心脏病,影响着贫困的热带人口. 早期手术可以改善结果, 但意识和可访问性仍然是关键挑战.
科学领域:
- 心脏病学
- 热带医学
- 公共卫生
背景情况:
- 心脏内膜纤维化 (EMF) 是一种被忽视的热带疾病,在低收入国家普遍存在.
- 以内心纤维组织沉积为特征,导致限制性生理和心力衰竭.
研究的目的:
- 总结目前对热带内肌纤维化的理解.
- 突出疾病的特征,自然史和管理挑战.
主要方法:
- 对心脏内膜纤维化现有文献的审查.
- 流行病学,病因学和临床数据的综合.
主要成果:
- 影响热带地区 (非洲,亚洲,南美) 的农村人口.
- 原因可能包括饮食,环境和传染因素的结合.
- 这种疾病从活跃的炎症阶段发展为慢性限制性心力衰竭,通常伴有风.
- 预后很差, 手术选择有限.
结论:
- 提高医疗保健专业人员和政策制定者的意识对于制定有效的预防和治疗策略至关重要.
- 包括手术在内的可及及及时的干预措施是改善患者的结果所必需的.
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