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Updated: Jul 29, 2025

Forskolin-induced Swelling in Intestinal Organoids: An In Vitro Assay for Assessing Drug Response in Cystic Fibrosis Patients
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高效CFTR调节器后的气道清除:使生命正常化并减少治疗负担

Danielle M Goetz1, Carla K Frederick2, Geovanny Perez1

  • 1Department of Pediatrics, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo, Buffalo, New York, USA.

Pediatric pulmonology
|May 26, 2023
PubMed
概括

许多患有囊性纤维化 (CF) 的人在开始高效的CFTR调制剂疗法 (HEMT) 后减少或停止呼吸道清除疗法 (ACT). 这种转变会影响CF护理团队的治疗决策.

关键词:
在CFTR调节器疗法中使用CFTR调节器.在CFTR调节器.呼吸道清除疗法治疗囊性纤维化症是什么

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