在患有神经肌肉疾病的患者中考虑呼吸系统问题
Nina Patel1, Ileana M Howard2,3, Ahmet Baydur4
1The Dornsife School of Arts, Letters and Sciences, University of Southern California, Los Angeles, California, USA.
神经肌肉疾病 (NMDs) 导致呼吸系统受损,导致呼吸困难和感染. 先进的呼吸系统支持改善了患者的生活质量和寿命.
科学领域:
- 神经学 神经学
- 肺部病理学 肺部病理学
- 呼吸系统医学 呼吸系统医学
背景情况:
- 神经肌肉疾病 (NMDs) 逐渐削弱呼吸道肌肉.
- 这导致肺功能减弱,咳受损,感染风险增加.
- 由于肌肉衰弱或中央控制问题,睡眠呼吸障碍很常见.
研究的目的:
- 概述NMDs中的呼吸道并发症.
- 描述呼吸系统损伤的评估方法.
- 讨论呼吸辅助的管理策略和技术进步.
主要方法:
- 评估坐着和躺着的生命能力 (VC).
- 测量呼吸道肌肉的强度.
- 评估咳有效性和睡眠研究.
主要成果:
- 呼吸道肌肉衰弱显著影响肺功能和气道清除.
- 对于移动性和独立性而言,非侵入性通风是首选的.
- 气管切除术只适用于严重的腹筋损伤和失败的咳辅助.
结论:
- 呼吸支的技术进步提高了NMD患者的生活质量和生存率.
- 家庭护理是最优的,但对护理人员来说存在重大挑战.
- 多因素决定指导启动辅助通风.
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