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Updated: Jul 27, 2025

Increasing Pulmonary Artery Pulsatile Flow Improves Hypoxic Pulmonary Hypertension in Piglets
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[遗传性肺高血压家族与遗传性肺高血压家族

Y K Lin1, D H Yang1, C Lei1

  • 1Department of Pulmonary and Critical Care Medicine, the Second Xiangya Hospital, Central South University, Changsha 410011, China.

Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseases
|June 6, 2023
PubMed
概括

这项研究确定了一种BMPR2基因变异,导致遗传性肺高血压 (HPAH) 在怀疑遗传性出血端膜病 (HHT) 的家庭. 遗传分析证实了导致蛋白质功能障碍的特定突变,强调了家族病史和HPAH和HHT遗传检测的重要性.

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