自免疫多腺体综合征3型与IgG4相关疾病复杂
Yusuke Murata1, Masaki Haneda1, Nobukazu Miyakawa1
1Department of Diabetes, Metabolism and Endocrinology, Kumamoto University Hospital, Japan.
Internal medicine (Tokyo, Japan)
|June 21, 2023
概括
这项研究报告了一例罕见的日本女性自身免疫多腺体综合征3A型 (APS-3A) 病例,该病例与1型糖尿病,自身免疫甲状腺疾病和IgG4相关疾病 (IgG4-RD) 一起发生. 在不使用类固醇的情况下,IgG4-RD的手术干预成功.
科学领域:
- 内分泌学 在内分泌学.
- 免疫学 免疫学 免疫学
- 类风湿病学 类风湿病学
背景情况:
- 自免疫多腺综合征3A型 (APS-3A) 是一种罕见的疾病,其特征是自身免疫性甲状腺疾病 (AITD) 和1型糖尿病 (T1DM).
- 免疫球蛋白G4相关疾病 (IgG4-RD) 是一种可以影响各种器官的纤维炎症疾病.
- APS和IgG4-RD的共存非常罕见,特别是在亚洲人群中.
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