在家族地中海热病中胺激素升高:来自青少年炎症性风湿症队列的一项研究

Nabiha Sbeih1, Rim Bourguiba2, Nadia Hoyeau-Idrissi3

  • 1Department of Internal Medicine, National Reference Centre for Auto-inflammatory Diseases and inflammatory Amyloidosis (CEREMAIA), Tenon Hospital, AP-HP, Paris, France; Sorbonne Université, Inserm U938, Paris, France; Laboratory of Molecular mechanisms of Hematological disorders and therapeutic implications, INSERM U1163 and CNRS ERL 8254, Fondation Imagine, Paris, France.

概括

家庭地中海热 (FMF) 患者经常表现出巨细胞 (MC) 激活的症状,血液和尿液中观察到胺水平升高. 这表明MCs在FMF病理生理学中可能发挥作用,即使是用素治疗.

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