单边兰布形头骨同位症的前面面部特征:一个多中心评估
Jonathan Lee1, Sanjay Naran2,3,4, Daniel Mazzaferro5
1From the Division of Plastic and Reconstructive Surgery, Baystate Health System, Springfield, Mass.
Plastic and reconstructive surgery. Global open
|June 26, 2023
概括
单边的羊毛状骨头结症呈现出明显的面部特征,包括一个升高的双侧耳朵和对侧 parietal bossing. 这些前面面部特征有助于将其与变形性脑相区分开来.
科学领域:
- 面外科手术 面外科手术
- 儿科神经外科 儿科神经外科
- 整形外科 整形外科 整形外科
背景情况:
- 单侧羊状骨突变 (ULC) 是一种复杂的疾病,常常与变形性脑症混为一谈.
- 诊断通常依赖于头骨成像和后部/鸟眼视图,但前面特征的理解较少.
- 面部评估提供了一个潜在的更简单的诊断方法,由于减少阻塞.
研究的目的:
- 描述非综合征性单边羊毛状骨突. 描述非综合征性单边羊毛状骨突. 描述非综合症性单边羊毛状骨突.
- 识别在手术前照片上可见的关键诊断特征.
主要方法:
- 对患有孤立的ULC的患者进行回顾性队列审查.
- 对手术前的额头和个人资料照片进行分析,以寻找突出的面部特征.
主要成果:
- 分析了19名非综合征患者 (11左,8右ULC).
- 关键的发现包括更大的ipsilateral耳朵可见性,对侧面的顶侧面 bossing,和轻微的对侧面的正面 bossing.
- 患者表现出高高的轨道,变化的头,以及C形面部脊椎病,鼻根和下巴的逆侧偏差.
结论:
- ULC的标志性前面面部特征包括双侧耳视力,对侧头顶侧,双侧面脊柱.
- 这些特征可能与巨突起的移位有关,有助于诊断.
- 需要进一步的研究来评估术后这些面部特征的长期纠正.
相关概念视频
Cranial Bones: Lateral View
2.4K
The lateral view of the cranium is dominated by temporal, sphenoid, and ethmoid bones.
The temporal bone forms the lower lateral side of the skull. The temporal bone is subdivided into several regions. The flattened upper portion is the squamous portion of the temporal bone. Below this area and projecting anteriorly is the zygomatic process of the temporal bone, which forms the posterior portion of the zygomatic arch. Posteriorly is the mastoid portion of the temporal bone. Projecting...
The temporal bone forms the lower lateral side of the skull. The temporal bone is subdivided into several regions. The flattened upper portion is the squamous portion of the temporal bone. Below this area and projecting anteriorly is the zygomatic process of the temporal bone, which forms the posterior portion of the zygomatic arch. Posteriorly is the mastoid portion of the temporal bone. Projecting...
2.4K
Cranial Bones: Superior and Posterior View
2.4K
The superior view of the cranium shows the frontal and paired parietal bones.
The frontal bone is the single bone that forms the forehead. At its anterior midline, between the eyebrows, there is a slight depression called the glabella. The frontal bone also forms the supraorbital margin of the orbit. Near the middle of this margin is the supraorbital foramen, the opening that provides passage for a sensory nerve to the forehead. The frontal bone is thickened just above each supraorbital margin,...
The frontal bone is the single bone that forms the forehead. At its anterior midline, between the eyebrows, there is a slight depression called the glabella. The frontal bone also forms the supraorbital margin of the orbit. Near the middle of this margin is the supraorbital foramen, the opening that provides passage for a sensory nerve to the forehead. The frontal bone is thickened just above each supraorbital margin,...
2.4K
Assessment of Airway, Skin Color, and Use of Accessory Muscles
1.0K
A thorough assessment of respiratory health is paramount in clinical settings to identify and manage respiratory distress and ensure adequate oxygenation. This article elaborates on the critical aspects of respiratory evaluation, including airway assessment, skin color examination, and the observation of accessory muscle use, which are integral to effectively diagnosing and managing patients with respiratory conditions.
Introduction
The initial evaluation of a patient's respiratory system...
Introduction
The initial evaluation of a patient's respiratory system...
1.0K
Sutures of the Skull
7.0K
The human skull is composed of several bones that come together to protect the brain and support the structures of the face. The junctions where these bones meet are called sutures.
Sutures are immobile joints between adjacent bones of the skull. The narrow gap between the bones is filled with dense, fibrous connective tissue that unites the bones. The long sutures located between the skull bones are not straight but instead follow irregular, tightly twisting paths. These twisting lines tightly...
Sutures are immobile joints between adjacent bones of the skull. The narrow gap between the bones is filled with dense, fibrous connective tissue that unites the bones. The long sutures located between the skull bones are not straight but instead follow irregular, tightly twisting paths. These twisting lines tightly...
7.0K


