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在佩病中,GAA缺乏会破坏远端气道细胞

Léa El Haddad1, Elias Lai1, Preetish Kadur Lakshminarasimha Murthy2

  • 1Division of Pulmonary and Sleep Medicine, Department of Pediatrics, School of Medicine, Duke University, Durham, North Carolina, United States.

American journal of physiology. Lung cellular and molecular physiology
|June 27, 2023
PubMed
概括

庞佩氏病会导致肺细胞中糖原的积累,损害表面活性剂的产生,并加剧呼吸系统问题. 这项研究揭示了对膜细胞的新影响,有助于佩病呼吸不全.

关键词:
庞贝病是庞贝病的一种疾病.遥远的气道细胞.呼吸系统功能障碍 呼吸系统功能障碍表面活性蛋白质的表面活性蛋白质.

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