基库奇-藤本病:一个全面的审查
Vikram K Mahajan1, Vikas Sharma2, Neeraj Sharma2
1Department of Dermatology, Venereology and Leprosy, Dr. Radhakrishnan Government Medical College, Hamirpur 177001, Himachal Pradesh, India. vkm1@rediffmail.com.
World journal of clinical cases
|June 29, 2023
概括
基库奇-富士门氏病 (KFD) 是一种罕见的,自我限制的淋巴结疾病,影响年轻成年人. 诊断需要仔细的组织病理学,因为KFD可以模仿其他疾病,如淋巴瘤和狼.
科学领域:
- 免疫学 免疫学 免疫学
- 病理学 病理学 病理学
- 类风湿病学 类风湿病学
背景情况:
- 基库奇-富士门氏病 (KFD) 是一种罕见的,良性,自我限制的死结性淋巴腺炎,原因不明.
- 它主要影响年轻成年人,发烧和淋巴腺病变,并可能有皮肤表现.
- KFD与系统性红斑狼 (SLE) 有着复杂的关系,并且经常被误诊.
研究的目的:
- 审查KFD的临床流行病学,诊断和管理方面.
- 突出KFD的诊断挑战和差异诊断.
- 为管理KFD的执业临床医生提供见解.
主要方法:
- 对临床流行病学数据的审查.
- 对诊断方式的分析,包括他的病理学.
- 评估当前的管理策略.
主要成果:
- 在30%-40%的病例中,KFD表现为发烧和淋巴腺病变,可变的皮肤干扰.
- 不同诊断包括淋巴瘤,SLE和传染性淋巴腺炎.
- 精细针吸入细胞学通常是不特定的; 组织病理学是诊断的.
结论:
- 确切的KFD诊断依赖于淋巴结活检的仔细的组织病理学评估.
- 早期活检至关重要,以避免不必要的调查和经验治疗.
- 管理,通常是经验性的,可能涉及皮质类固醇或氧化.
相关概念视频
Inflammatory Bowel Disease I: Ulcerative Colitis
226
Introduction
Inflammatory bowel disease, or IBD, encompasses a group of disorders characterized by chronic inflammation or ulceration of the gastrointestinal tract.
Risk Factors
The exact cause of IBD remains unclear, although it is believed to be due to a mix of genetic, environmental, microbial, and immune factors. Genetic factors are significant in determining susceptibility to IBD, with family history being a critical risk factor. Individuals with a first-degree relative who has IBD are at...
Inflammatory bowel disease, or IBD, encompasses a group of disorders characterized by chronic inflammation or ulceration of the gastrointestinal tract.
Risk Factors
The exact cause of IBD remains unclear, although it is believed to be due to a mix of genetic, environmental, microbial, and immune factors. Genetic factors are significant in determining susceptibility to IBD, with family history being a critical risk factor. Individuals with a first-degree relative who has IBD are at...
226
Inflammatory Bowel Disease II: Crohn's Disease
303
Introduction
Inflammatory bowel disease, commonly known as IBD, refers to a collection of disorders that lead to persistent inflammation of the gastrointestinal tract. The two types of IBD are ulcerative colitis, which impacts the colon, and Crohn's disease, which can involve any part of the gastrointestinal segment.
Crohn's disease
Crohn's disease is a chronic, systemic inflammatory bowel disease (IBD) that predominantly affects the gastrointestinal tract. It is marked by...
Inflammatory bowel disease, commonly known as IBD, refers to a collection of disorders that lead to persistent inflammation of the gastrointestinal tract. The two types of IBD are ulcerative colitis, which impacts the colon, and Crohn's disease, which can involve any part of the gastrointestinal segment.
Crohn's disease
Crohn's disease is a chronic, systemic inflammatory bowel disease (IBD) that predominantly affects the gastrointestinal tract. It is marked by...
303
Chronic Bowel Disorders: Introduction
490
Chronic bowel diseases are a group of long-term conditions affecting the digestive tract, characterized by inflammation and damage to the gut lining. These conditions primarily include irritable bowel syndrome and inflammatory bowel disease.
Irritable Bowel Syndrome (IBS) is a common disorder affecting the gastrointestinal tract. The distinctive feature is recurrent abdominal pain associated with altered bowel movements, manifesting as constipation, diarrhea, or fluctuating between both. The...
Irritable Bowel Syndrome (IBS) is a common disorder affecting the gastrointestinal tract. The distinctive feature is recurrent abdominal pain associated with altered bowel movements, manifesting as constipation, diarrhea, or fluctuating between both. The...
490
Nephrotic Syndrome II : Assessment and Medical Management
10
IntroductionNephrotic syndrome is a kidney disorder marked by excessive protein loss in the urine, leading to various systemic complications. This condition often results from damage to the glomeruli—the kidney's filtering units—causing proteinuria, low blood protein levels, and fluid retention. Understanding the assessment, diagnosis, and management of nephrotic syndrome is essential for effective treatment and prevention of further kidney damage.AssessmentPatient History: Document...
10
Nephrotic Syndrome I : Introduction
10
Nephrotic Syndrome is a chronic kidney disorder defined by clinical findings such as severe proteinuria, hypoalbuminemia, hyperlipidemia, and edema. These symptoms result from damage to the glomeruli, the kidney’s filtering units, increasing their permeability to proteins.Definition and Meaning:Proteinuria, defined as the loss of more than 3.5 grams of protein per day in adults, is a crucial feature of nephrotic syndrome. This condition is often accompanied by edema, the accumulation of...
10
Irritable Bowel Syndrome II: Clinical Features and Diagnostic Evaluation
199
Irritable Bowel Syndrome II: Clinical Features and Diagnostic Evaluation
Irritable Bowel Syndrome (IBS) is classified into subtypes based on the predominant bowel habits as determined by the Bristol Stool Form Scale (BSFS). The subtypes are:
Irritable Bowel Syndrome (IBS) is classified into subtypes based on the predominant bowel habits as determined by the Bristol Stool Form Scale (BSFS). The subtypes are:
199


