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Updated: Jul 24, 2025

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线粒体复合体I组装中的组织特异性差异是由ECSIT中的新型ENU突变揭示出来的

Thomas Nicol1,2, Sara Falcone1,3, Andrew Blease1

  • 1Mammalian Genetics Unit, MRC Harwell Institute, Becquerel Avenue, Didcot, OX11 0RD, Oxfordshire, UK.

Cardiovascular research
|July 3, 2023
PubMed
概括

在ECSIT蛋白的突变影响线粒体复合体I组装,特别是在高能耗组织如心脏,导致心脏功能障碍. 这突出了线粒体功能中的组装因子的特定组织作用.

关键词:
一个心脏病患者的心脏病.综合体I 是一个综合体.心灵的心脏心脏的心脏心脏心脏线粒体中的线粒体.

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