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Updated: Jul 21, 2026

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研究患有法布里病的患者的骨矿物质密度和酶替代疗法的变化

Yuma Nose1, Hideki Fujii1, Shunsuke Goto1

  • 1Division of Nephrology and Kidney Center, Kobe University Graduate School of Medicine, Kobe, Japan.

Molecular genetics and metabolism
|July 5, 2023
PubMed
概括

在法布里病 (FD) 患者中,骨矿物质密度 (BMD) 与全球基素 (lyso-Gb3) 水平有关,特别是在男性中. 酶替代疗法 (ERT) 改善了男性的BMD,这表明Gb3积累会影响骨健康.

关键词:
骨矿物质密度 骨矿物质密度酶替代疗法是一种酶替代疗法.费布里病是什么意思 费布里病是什么意思这就是Lyso-Gb3的原因.

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Bone Disorders01:29

Bone Disorders

Aging and its effect on bone remodeling is the most common cause of bone disorders. In young and healthy people, bone deposition and resorption happen at an equal rate to maintain optimal bone health.
Bone deposition is also affected by the levels of sex hormones like estrogen and testosterone that promote osteoblast activity and bone matrix synthesis. When the level of these hormones decreases due to aging, it causes a reduction in bone deposition. As a result, bone resorption by osteoclasts...