门性高血压由二次血色变异引起的耐火性炎
Jun Tie1, Wen Yuan Jia1, Xiaoyuan Gou1
1State Key Laboratory of Cancer Biology, National Clinical Research Center for Digestive Diseases and Xijing Hospital of Digestive Diseases, Xijing Hospital, Air Force Medical University, Xi'an, Shaanxi, China.
Journal of clinical and translational hepatology
|July 6, 2023
概括
这一案例突出显示了骨质疏松症和血色素变异症之间罕见的关联,导致门门高血压和耐火性. 跨内肝移植系统 (TIPS) 有效地治疗了,强调了骨质疏松症患者的铁负荷监测.
科学领域:
- 血液学 血液学 血液学
- 肝病学 肝病学是一种肝病学.
- 胃肠病学 胃肠病学
背景情况:
- 骨质疏松症是一种罕见的遗传性疾病,其特点是骨质细胞功能受损和骨再吸收.
- 由于频繁输血红细胞,二次血红色素病可能会发展,导致铁过载.
- 门高血压是一种严重的并发症,可以由各种肝脏疾病引起.
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