爆发性肺:左心室非收缩性心肌病的病例和审查
Paula J Watts1,2, Oliver S Garbo1,2, Wendy Barrett1,2
1Department of Internal Medicine, Sky Ridge Medical Center, Lone Tree, CO.
HCA healthcare journal of medicine
|July 10, 2023
概括
左心室非紧缩性心肌病,一种罕见的心肌疾病,由于更好的成像,越来越多地被诊断出来. 管理与其他心肌病症保持一致,病例报告突出其呈现.
科学领域:
- 心脏病学 心脏病学
- 遗传学 遗传学 是一个
- 病理学 病理学 病理学
背景情况:
- 左心室非紧缩性心肌病 (LVNC) 是一种罕见的先天性心肌疾病.
- 它是胚胎发生过程中心肌发育异常的结果,导致突出的心室轨道.
- 临床表现非常不同,从无症状病例到严重的心律失常和心力衰竭.
研究的目的:
- 审查目前对左心室非紧缩性心肌病的理解.
- 在患有急性心力衰竭的年轻成年人中呈现LVNC的临床病例.
- 强调提高对这种疾病的认识和诊断能力的重要性.
主要方法:
- 关于左心室非紧缩性心肌病的文献综述.
- 一个38岁的男性患有突发性肺的案例研究介绍.
- 心声学和临床数据分析.
主要成果:
- 患者被诊断为左心室非紧缩性心肌病.
- 该病例说明了LVNC的严重表现,伴有闪发性肺.
- 审查证实LVNC的诊断不足,但随着诊断的改善,患病率正在增加.
结论:
- 左心室非收紧性心肌病需要高度的临床怀疑.
- 早期诊断和适当的治疗,类似于其他心肌病,至关重要.
- 这种情况虽然罕见,但显著影响心脏功能和患者的预后.
相关概念视频
Cardiomyopathy IV: Restrictive Cardiomyopathy
12
Restrictive cardiomyopathy (RCM) is a rare heart muscle disease characterized by impaired ventricular filling due to stiffened ventricular walls, leading to significant diastolic dysfunction.EtiologyRestrictive cardiomyopathy can arise from both inherited and acquired diseases, many of which are systemic. It is categorized into four main types: infiltrative, storage, non-infiltrative, and endomyocardial diseases.Infiltrative diseases, such as amyloidosis, lead to RCM by depositing amyloid...
12
Cardiomyopathy II: Dilated Cardiomyopathy
11
Dilated cardiomyopathy, or DCM, is a progressive myocardial disorder characterized by ventricular chamber dilation and contractile dysfunction.EtiologyVarious factors can cause DCM, including hypertension and heavy alcohol intake, which contribute to the weakening and enlargement of the heart muscle. Viral infections, such as Coxsackievirus B, adenoviruses, and influenza, can lead to DCM by causing inflammation and damage to heart tissue. Certain chemotherapeutic agents, including daunorubicin,...
11
Cardiomyopathy III: Hypertrophic Cardiomyopathy
16
Hypertrophic cardiomyopathy, or HCM, is an autosomal dominant genetic disorder characterized by asymmetric left ventricular hypertrophy without ventricular dilation. It is more common in men and is typically diagnosed in young, athletic adults.EtiologyHCM is primarily genetic and is caused by mutations in genes encoding sarcomeric proteins. Researchers have identified over 1400 mutations across at least 11 different genes. Among these, the most frequently occurring mutations are found in the...
16
Cardiomyopathy I: Introduction and Classification
19
Cardiomyopathy, or CMP, is a group of diseases affecting the myocardial structure, impairing its ability to pump blood effectively. This condition can lead to arrhythmias, heart failure, or sudden cardiac death.Cardiomyopathies are classified into primary and secondary categories:Primary Cardiomyopathy refers to conditions involving only the heart muscle that are often idiopathic (of unknown cause) or genetic. They primarily affect the myocardium without the involvement of other systemic...
19
Imbalances in Cardiac Output
1.4K
The heart's primary function is to pump blood throughout the body, maintaining a balance between blood sent out (cardiac output) and blood returning (venous return). If this balance is disrupted, it can result in congestive heart failure (CHF), a severe condition where the heart becomes an inefficient pump, leading to inadequate blood circulation.
CHF can occur due to the failure of either side of the heart. Left-side failure leads to pulmonary congestion—the right side continues to send...
CHF can occur due to the failure of either side of the heart. Left-side failure leads to pulmonary congestion—the right side continues to send...
1.4K
Aortic Regurgitation II: Clinical Features and Diagnostic Tests
32
Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...
32


