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酶替代疗法对佩病晚期发作的骨密度的影响

Mahima Avanti1, Angela Martin1, Rod Carlo Columbres1

  • 1Division of Genetics, Department of Pediatrics, University of California - Irvine, Orange, CA 92697, United States of America.

Molecular genetics and metabolism
|July 29, 2023
PubMed
概括

酶替代疗法 (ERT) 可能改善晚发佩病 (LOPD) 患者的骨矿物质密度 (BMD). 这项研究发现ERT与增加的BMDZ-score相关,这表明它对骨质疏松症有保护作用.

关键词:
葡萄糖化酶αα的使用.骨矿物质密度 骨矿物质密度德克萨 (DEXA) 是一个双能量X射线吸收度测量酶替代疗法是一种酶替代疗法.晚期发病的庞贝病 晚期发病的庞贝病

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