:

Simone Petrarulo1, Manuel Lucchin2, Stefano Oldani3

  • 1Respiratory Disease Unit, Department of Cardiac Thoracic, Vascular Sciences and Public Health, University of Padova, Padova, Italy.

Frontiers in medicine
|August 4, 2023
PubMed
概括

一种罕见的遗传性疾病, lysinuric 蛋白质不耐受 (LPI),导致严重的肺部疾病 (肺膜蛋白质). 全肺洗 (WLL) 成功治疗了这种危及生命的呼吸衰竭,提供了一个新的治疗选择.