[肺膜微病:关于摩洛哥两例家族病例的报告]
Revue des maladies respiratoires
|August 5, 2023
概括
肺膜微病 (PAM) 是一种罕见的遗传性肺病. 通过成像和支气管支气管洗的早期诊断对于管理这种情况至关重要,肺移植作为主要治疗方法.
科学领域:
- 肺部病理学 肺部病理学
- 放射学 放射学是一门学科.
- 遗传学 是一个遗传学.
背景情况:
- 肺膜微病 (PAM) 是一种罕见的自体逆向性疾病.
- 通常是无症状的,PAM通常是在例行放射学检查中发现的.
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