患有状细胞贫血的儿童的黄:基于病例的方法
Srinivas Srinidhi Vadlapudi1, Anshu Srivastava2, Praveer Rai3
1Department of Pediatric Gastroenterology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India.
Indian journal of pediatrics
|August 9, 2023
概括
患有黄的状细胞贫血 (SCA) 患者需要谨慎管理,因为状细胞肝病症等潜在并发症. 一个逐步的方法和多学科的团队对于高风险的个人至关重要.
科学领域:
- 血液学 血液学 血液学
- 胃肠病学 胃肠病学
- 儿科 儿科 儿科
背景情况:
- 细胞贫血 (SCA) 是一种遗传性血液疾病,影响β环球蛋白基因,导致10-40%患者肝胆道系统的并发症.
- SCA患者的黄可能源于多因素的原因,包括血管封闭性危机 (VOC) 诱导的状细胞肝病,胆病,病毒性肝炎和血染色症.
- 在SCA患者中,各种肝病的临床重叠和共存带来了诊断挑战.
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