[临床上氨基性皮肤肌炎:一种与急性和严重的间歇性肺病相关的罕见实体]
Camille Debrus1, Doriane Calmes1, Christian Von Frenckell2
1Service de Pneumologie, CHU Liège, Belgique.
Revue medicale de Liege
|August 10, 2023
概括
皮肤肌肉炎是一种罕见的炎症性疾病,可能涉及肺部. 高抗黑色素瘤分化关联基因5 (抗MDA5) 抗体水平表明严重,快速进展的肺部疾病,即使没有肌肉炎症.
科学领域:
- 类风湿病学 类风湿病学
- 肺部病理学 肺部病理学
- 免疫学 免疫学 免疫学
背景情况:
- 皮质肌炎是一种罕见的自身免疫性疾病,引起肌肉炎症和皮肤皮疹.
- 它可以影响多个器官,心脏,肺和关节的参与往往表明预后不佳.
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