阴性冷血红蛋白尿:儿童患者的诊断困境
Keenan O Hogan1, Gabor Oroszi2
1Department of Pathology and Laboratory Medicine, University of Kansas Medical Center, Kansas City, Kansas, USA.
Transfusion medicine (Oxford, England)
|August 13, 2023
概括
在儿童中诊断阳性冷血红蛋白尿症 (PCH) 是具有挑战性的,因为复杂的自身免疫解血性贫血呈现. 唐纳-兰德斯坦纳测试对于识别导致PCH的特定双相血解素至关重要.
科学领域:
- 儿科血液学 儿科血液学
- 自身免疫性疾病 自身免疫性疾病
- 输血医学 输血医学
背景情况:
- 自免疫血清性贫血 (AIHA) 在儿童中很少见,具有多种诊断方法.
- 透性冷血红蛋白尿 (PCH) 是一种不常见的AIHA亚型,需要进行特定的诊断测试.
- 鉴定致病的双相血解素是准确的PCH诊断的关键.
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