-:2.

C A P F Alves1, J Sidpra2,3, A Manteghinejad4

  • 1From the Division of Neuroradiology (C.A.P.F.A., A.M., S.R.T., S.A., M.T.W.), Department of Radiology, Children's Hospital of Philadelphia, Philadephia, Pennsylvania alvesc@chop.edu.

概括

丹迪-沃克表型患者的大脑干发育不全存在轻度和严重的形式. 严重形式的特征是体形,与更糟糕的临床结果和更高的死亡率有关.