与胃内源性囊相关的胃内膜封存:胃肺! 这是一个巨大的惊喜!
Khyati Kiran Janapareddy1, Nitin James Peters1, Ram Samujh1
1Department of Pediatric Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Indian journal of thoracic and cardiovascular surgery
|August 23, 2023
概括
我们介绍了一个罕见的乳腺内膜封存 (ILS) 病例,与乳腺内膜囊同时发生,该病例发生在患有复发性血栓塞的婴儿身上. 手术切除证实了这两种异常,突出了这种极其罕见的先天性疾病.
科学领域:
- 儿科手术 儿科手术
- 胸部外科手术 胸部外科手术
- 遗传异常是一种先天性异常.
背景情况:
- 内膜隔离 (ILS) 是一种罕见的先天性肺形.
- 肠道性囊与ILS的同时存在是非常罕见的,报告的病例很少.
- 血和复发性肺炎是ILS的潜在临床表现.
研究的目的:
- 报告一个极为罕见的婴儿同时发生腹腔内隔离和肠源性囊的情况.
- 描述这种罕见疾病的诊断和治疗方法.
- 审查关于同时存在的ILS和肠道囊的现有文献.
主要方法:
- 一个6个月大的男婴患有血栓塞的案例介绍.
- 诊断评估包括成像,以确定肺部巩固,伪动脉瘤和脊柱异常.
- 涉及ILS胸腔镜切除的手术干预,随后进行胸腔切除以切除肠道囊.
主要成果:
- 婴儿呈现出血栓塞并被诊断为ILS,肺动脉伪动脉瘤和脊柱裂.
- 最初的胸腔镜切除证实了ILS.
- 随后需要进行胸切除术,以切除因复发性血而导致的含有胃粘膜的同时存在的肠道性囊.
结论:
- 同时发生的腹膜内膜隔离和肠产囊是一种极其罕见的先天性异常.
- 这一案例强调了对复杂的先天性肺形并存病理的彻底评估的重要性.
- 成功的手术治疗包括分阶段切除内隔离和肠道性囊.
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