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Updated: Jul 17, 2025

Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle
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线粒体脂肪酸合成中的缺陷会损害铁代谢,并导致胺水平升高

Debdeep Dutta1,2, Oguz Kanca1,2, Seul Kee Byeon3

  • 1Department of Molecular and Human Genetics, Baylor College of Medicine, Houston, TX, USA.

Nature metabolism
|August 31, 2023
PubMed
概括

线粒体脂肪酸合成 (mtFAS) 酶Mecr对于预防神经退行至关重要. 失去Mecr会破坏铁和胺代谢,导致和人类的神经退行性表型.

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