Sheila K Pierson1, Megan S Lim2, Gordan Srkalovic3

  • 1Department of Medicine, Center for Cytokine Storm Treatment & Laboratory, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA.

Blood advances
|September 1, 2023
PubMed
概括

现实世界的数据表明,抗干白素6 (IL6) 疗法是异常多中心卡斯特曼病 (iMCD) 的有效一线治疗方法. 细胞毒性化疗对严重病例有好处,而皮质类固醇单一治疗对iMCD患者的疗效有限.

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