在诊断,治疗和管理Papillon-Lefèvre综合征的最新进展
Roza Haghgoo1, Majid Mehran1, Morteza Banakar2,3
1Department of Pediatric Dentistry, Faculty of Dentistry, Shahed University, Tehran, Iran.
Evidence-based dentistry
|September 7, 2023
概括
帕皮隆 - 莱弗勒综合征 (PLS) 治疗的成功取决于早期诊断和积极的管理. 多学科的方法,包括及时拔牙,卫生,专业护理和抗生素,可以减缓牙周炎的进展.
科学领域:
- 牙周病学 牙周病学
- 遗传学 是一个遗传学.
- 口腔医学是指口腔医学.
背景情况:
- 帕皮隆-莱费弗里综合征 (PLS) 是一种罕见的遗传性疾病,其特征是手掌植物性皮炎和严重的快速进展的牙周炎.
- 在PLS的牙周炎往往导致牙过早脱落,显著影响口腔功能和生活质量.
研究的目的:
- 系统地审查临床研究关于牙周治疗在患有帕皮隆-莱弗勒综合征 (PLS) 患者的成功.
- 确定有助于成功的牙周病患者治疗结果的关键因素.
主要方法:
- 在PubMed,LIVIVO和Ovid进行了系统的文献搜索,截至2021年3月.
- 包括的研究报告了PLS患者的成功治疗结果 (≤4颗永久牙丢失,牙周炎停止或探针深度≤5毫米,≥24个月的随访).
- 提取的数据包括诊断,人口统计,牙周参数,治疗方法以及9名PLS患者的12项研究的结果.
主要成果:
- 成功的牙周治疗与及时拔牙,严格遵守口腔卫生,定期进行专业的除牙和支持性牙周护理有关.
- 辅助全身抗生素治疗和抑制Aggregatibacter actinomycetemcomitans低于检测限值与疾病进展停止和牙周稳定有关.
结论:
- 一种密集的,多学科的方法,严格遵守患者的要求,对于减缓PLS相关牙周炎进展至关重要.
- 早期诊断PLS和控制A. actinomycetemcomitans对于成功的治疗结果至关重要.
- 强调及时干预,始终保持口腔卫生,定期接受专业护理以及明智地使用抗生素.
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