患有多变性心肌病症的儿童心电图异常的模式
Mayme Marshall1, Aneeq Malik2, Maully Shah3
1Cleveland Clinic Children's Hospital, Cleveland, OH, USA.
Pediatric cardiology
|September 8, 2023
概括
超心肌病 (HCM) 的儿童的心电图 (ECG) 经常显示出超出典型超的异常. 这些发现,包括应变模式和Q波,需要进一步对心声回声图进行评估,以便早期诊断.
科学领域:
- 儿童心脏病学 儿童心脏病学
- 心血管研究研究心血管研究
- 诊断性心电图谱 诊断性心电图谱
背景情况:
- 增高性心肌病变 (HCM) 是儿童发病率和死亡率的重要原因.
- 早期识别和治疗儿科HCM至关重要.
- 电心电图 (ECG) 是对儿科心脏病的重要查工具,但HCM的模式尚不清楚.
研究的目的:
- 描述一大批患有多变性心肌病 (HCM) 的儿童和青少年的国际队列中的心电图 (ECG) 模式.
- 确定儿科HCM中常见和非典型的心电图异常.
- 评估心电图发现的有用性,以促使进一步的诊断评估.
主要方法:
- 来自国际儿科和青少年患者队列 (≤21岁) 诊断出HCM的482个ECG的回顾性审查.
- 对心电图发现的分析,包括左心室缩 (LVH),双心室缩 (BVH),应变模式和病理Q波.
- 电图异常与HCM诊断的相关性.
主要成果:
- 88%的儿科HCM患者表现出异常的心电图.
- 最常见的异常是左心室缩 (LVH) 或双心室缩 (BVH) (46%),通常具有菌株模式 (60%的LVH/BVH病例).
- 很大一部分患者 (9%) 呈现出孤立的应变模式,15%的患者呈现出孤立的病态Q波,突出显示了超出典型缩的心电图发现.
结论:
- 儿科超性心肌病经常呈现出多种ECG异常,包括那些不仅仅表明过度化的异常.
- 在儿童心电图上出现LVH,BVH,菌株模式或病态Q波的存在需要进一步调查.
- 儿科HCM的心电图发现对于早期检测至关重要,应该促使心电图评估来排除这种情况.
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