[血栓性血栓细胞衰竭紫外线 - 一个罕见的诊断]
Sigrun Einarsdottir1, Cecilia Rosander2, Sofia Frändberg3
1med dr, specialistläkare, sektionen för hematologi och koagulation, Sahlgrenska universitetssjukhuset, Göteborg.
概括
血栓性血栓塞性紫外线 (TTP) 是一种罕见的血液疾病,由低ADAMTS13活性引起. 早期诊断和用血交换,类固醇,rituximab和caplacizumab的治疗改善了患者的治疗结果.
科学领域:
- 血液学 血液学 血液学
- 血管生物学 血管生物学
- 免疫学 免疫学 免疫学
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